Nitisinone used to treat a disorder tyrosinemia type 1 (HT-1). HT-1 is usually found on the age of the baby and so require lifelong treatment. This condition is caused by a deficiency of a certain natural substance that is needed to break down nutrients (tyrosine) that are found in food.
This effect causes the accumulation of tyrosine and related substances in the liver. Nitisinone works by helping prevent the formation and accumulation of toxic substances which caused some damage to the liver, kidneys, and nervous system. This medication should be used along with a diet low in protein and tyrosine phenylalanine.
Take this medicine on an empty stomach at least 1 hour before a meal, usually twice daily, or as directed by a physician. For children who are unable to swallow capsules, the capsules may be opened and contents mixed in a small amount of water, formula, or apple immediately before use. Make sure the child swallow the whole dose.
The dosage is based on body weight, medical condition, and response to treatment. Manufacturers recommend that patients should not take more than 2 milligrams per day. Take this medication regularly and at the same time every day.
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